治療
口服或注射糖皮質(zhì)激素,可控制眼部癥狀和全身癥狀,但對(duì)第8對(duì)腦神經(jīng)癥狀很難奏效。可用潑尼松每天1~2mg/kg。最近報(bào)道,頸交感神經(jīng)切除術(shù)可緩解第8對(duì)腦神經(jīng)癥狀。當(dāng)有主動(dòng)脈瓣關(guān)閉不全且無明顯心力衰竭時(shí),行主動(dòng)脈瓣置換術(shù),可獲得較好療效,延緩心力衰竭的發(fā)生。一旦出現(xiàn)心力衰竭或消化道出血,則應(yīng)分別給予對(duì)癥治療。